Weber-Christian panniculitis and auto-immune disease: a case report.
نویسنده
چکیده
A case is described of Weber-Christian panniculitis accompanied by a gammaglobulin disturbance which preceded by five years the diagnosis of an autoimmune hepatitis and pancytopenia. Also associated was the onset of diabetes mellitus, found at necropsy to be related to pancreatic islet amyloid deposition. This case reinforces the view that Weber-Christian panniculitis may be an adipose response to a variety of immunological stimuli.
منابع مشابه
Idiopathic lobular panniculitis (Weber Christian disease): a case report.
Weber Christian disease, an idiopathic relapsing febrile subcutaneous and visceral panniculitis is a rare disease in children. We report a case of Weber Christian disease for he first time from Kanti Children's Hospital.
متن کاملWeber-Christian disease: a case report.
Weber-Christian disease is a rare and poorly understood disorder of the adipose tissue.1,2 The exact aetiopathogenesis of this condition is largely unknown and it is also called idiopathic lobular panniculitis.3 In 1892, Pfeifer first described the skin condition now known as Weber-Christian disease, or idiopathic lobular panniculitis.4,5 In 1925, Weber further depicted the syndrome as case of ...
متن کاملWeber Christian disease.
Weber Christian disease or idiopathic lobular panniculitis is a skin condition that features recurring inflammation in the fat layer of the skin. We report a case of a 17 year old boy with Weber Christian disease as its occurence is extremely rare with only sparse case reports available, who presented with eighteen-month history off fever with chills off and on, arthralgia predominantly of the ...
متن کاملSystemic Weber-Christian disease
SYNOPSIS A patient suffering from Weber-Christian panniculitis was found at necropsy to have similar lesions in the visceral adipose tissue. When the lesions occur internally, diagnosis during life is complicated by the difficulty of examining visceral adipose tissue and the disease may often go unrecognized, but patients suffering from Weber-Christian panniculitis should be investigated bearin...
متن کاملIasian Pacific Journal of Allergy and Immunology
Weber-Christian disease (WCD) is an inflammatory disease of subcutaneous fat first described in 1892. Panush et al. I analysed the clinical and laboratory features of WCD, including chronic relapsing fever with subcutaneous non-sup purative nodules predominantly on lower extremities, arthralgia or ar thritis and myalgia. The laboratory features were elevated erythrocyte sedimentation rate, an...
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ورودعنوان ژورنال:
- Journal of clinical pathology
دوره 29 2 شماره
صفحات -
تاریخ انتشار 1976